Ciężkie przewlekłe zakrzepowo-zatorowe nadciśnienie płucne po splenektomii z powodu sferocytozy wrodzonej — potrzeba długoterminowego nadzoru i ścisłej współpracy hematologów i kardiologów

We present the case of a 34-year-old female patient with severe pulmonary hypertension diagnosed > 15 years after splenectomy to emphasize need monitor patients for development chronic thromboembolic (CTEPH). The lack screening tests this group patients, as in described case, resulted serious clinical condition at time diagnosis. Without specialized treatment, probability her survival 5 was only 10%. Close collaboration between haematologists and cardiologists is mandatory management post-splenectomy Life-long surveillance needed these due risk CTEPH. program required.